This Article  • References  • Full text PDF  • Send to a friend  • Save in My Folder  • Save to citation manager  • Permissions  Citing Articles  • Contact me when this article is cited  Related Content  • Similar articles in this journal  Social Bookmarking   What's this?

EOIN F. GAFFNEY, MB, BCH
Department of Pathology University of Rochester Medical Center Rochester, NY 14642

Am J Dis Child. 1978;132(8):818.

	Since this article does not have an abstract, we have provided the first 150 words of the full text PDF and any section headings.

Sir.—Pick et al in their interesting article in the JOURNAL (131:682-686, 1977) described a case of agammaglobulinemia characterized by the absence of IgG, IgA, IgD, and the salivary "secretory component" associated with a plasma cell dyscrasia and amyloidosis. They include a summary of the findings in other cases of amyloidosis associated with agammaglobulinemia.

One report that they did not include was relevant to the subject. I refer to the article by Ziegler and Penny¹ in which they described the first reported case of X-linked hypogammaglobulinemia associated with amyloidosis. The patient, a 14-year-old boy, died of meningoencephalitis and its sequelae, and at autopsy amyloid was detected in the liver, thymus, tonsils, and kidney.

I would also like to correct an inaccuracy in the comment by Pick et al. They state that seven of ten cases discussed by Mawas et al² seem to have a "mixed pattern" of amyloid deposition . . . [Full Text PDF of this Article]

CiteULike    Connotea    Del.icio.us    Digg    Reddit    Technorati    Twitter     What's this?