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Picture of the Month
Hassib Narchi, MD;
Walter W. Tunnessen, Jr, MD
From the Al-Hasa Specialty Services Division, Saudi Aramco-Al-Hasa Health Center, Saudi Aramco Medical Services Organization, Mubarraz, Saudi Arabia.
Arch Pediatr Adolesc Med. 1999;153:425-426.
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| Since this article does not have an abstract, we have provided the first 150 words of the full text and any section headings. |
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A 10-YEAR-OLD boy who had normal developmental milestones except for a speech delay was referred for evaluation of an asymptomatic heart murmur. His parents, who are first cousins, have 2 other healthy children.
On physical examination, the child was well nourished and without dysmorphic features. The cardiac examination revealed a grade 2/6 systolic murmur at the left lower sternal border. His peripheral pulses were equal, and the blood pressure in all 4 extremities showed no abnormalities. Findings of the remainder of the examination were unremarkable.
A chest radiograph; echocardiogram; and serum calcium, magnesium, and electrolyte measures showed no abnormalities. A representative electrocardiogram is shown in Figure 1. An audiogram demonstrated severe sensorineural deafness in both ears.
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Figure 1.
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Denouement and Discussion: Jervell and Lange-Nielsen Syndrome (Long QT Syndrome)
Figure 1. An electrocardiogram shows a heart rate of 53 beats/min, with a QT interval of 0.6 seconds and a corrected QT . . . [Full Text of this Article]
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