Toxic epidermal necrolysis from graft-vs-host disease. Occurrence in a patient with thymic hypoplasia
J. R. McCarty, S. S. Raimer and M. Jarratt
An infant with diarrhea, failure to thrive, and a seborrhea-like skin
eruption was thought to have fatal familial Leiner's syndrome. Treatment
with nonirradiated plasma was followed by graft-vs-host disease and fatal
toxic epidermal necrolysis; thymic hypoplasia was found at autopsy.
Accurate diagnosis of immunodeficiency syndromes is essential to avoid
potentially harmful therapy.
