Congenital adrenal hypoplasia and hypogonadotropic hypogonadism

M. P. Golden, B. M. Lippe and S. A. Kaplan

A 19-year-old male patient with congenital adrenal hypoplasia and elevated plasma adrenocorticotropic hormone level was found to have gonadotropin deficiency. Other hypothalamic-pituitary functions were normal. A possible relationship between hypothalamic-pituitary dysfunction and development of the cytomegalic form of congenital hypoplasia of the adrenals is suggested.

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